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Article in Japanese
Abstract
Case Report
A surgically treated case of neurofibromatosis type 1 associated with pulmonary mucosa-associated lymphoid tissue lymphoma
Fumihiro Hommuraa Akihiko Tanakab Keisuke Yamaguchic Hiroe Itamid Kenji Akiea Yuichiro Fukasawad
aDepartment of Respiratory Medicine, Sapporo City General Hospital
bDepartment of Respiratory Surgery, Sapporo City General Hospital
cDepartment of Hematology, Sapporo City General Hospital
dDepartment of Diagnostic Pathology, Sapporo City General Hospital
ABSTRACT
A 59-year-old man had pneumothorax associated with giant emphysematous bullae in his right lung 4 years ago, and his pneumothorax improved after conservative treatment with a chest tube. A nodule was found in his right middle lung lobe by chest CT scanning during re-evaluation of the bullae. Neurofibromatosis type1 (NF1) was also diagnosed based on a characteristic skin rash and his family history. Although we suspected the nodule of being lung cancer prior to surgery, surgical pathology specimens revealed mucosa-associated lymphoid tissue (MALT) lymphoma. Pulmonary MALT lymphoma associated with NF1 has never been reported, and we considered this to be a rare case.
KEYWORDS
Neurofibromatosis type 1 Pulmonary MALT lymphoma
Received 25 Jul 2014 ／ Accepted 12 Feb 2015
AJRS, 4(3): 231-234, 2015
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