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Article in Japanese
Abstract
Original Article
Survey of the clinical characteristics and living conditions of patients with bronchiolitis obliterans using the data from Japan’s national registry
Naozumi Hashimotoa Koji Sakamotob Keiko Wakaharab
aDepartment of Respiratory Medicine, Fujita Health University
bDepartment of Respiratory Medicine, Nagoya University Hospital
ABSTRACT
Bronchiolitis obliterans (BO) is an intractable lung disease that causes respiratory failure. Due to growing awareness of BO in Japan, it was registered as a designated intractable disease. The aim of this study was to determine the clinical characteristics and living conditions of patients with BO by analyzing Japan’s national data on patients with designated intractable diseases. Through the combined data from 15 newly certified individuals and 36 re-certified individuals (selected from a total of 91 sets of data from individual clinical survey forms) we determined the typical clinical characteristics of BO. Idiopathic BO is a rare intractable lung disease. These data encourage us to construct a comprehensive registry for both idiopathic BO and secondary BO due to transplantation, hematologic malignancies, and collagen diseases.
KEYWORDS
Bronchiolitis obliterans (BO) Designated intractable disease Clinical registry form Respiratory function test Constrictive bronchiolitis
Received 17 Mar 2023 ／ Accepted 18 May 2023
AJRS, 12(5): 240-245, 2023
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