The 2022 revised diagnostic criteria for IgG4-related respiratory disease
Tomohiro Handaa,b Shoko Matsuic Hiroshi Yamamotod Yuko Wasedae Tae Iwasawaf Takeshi Johkohg Kenji Notoharah Akira Hebisawai
aDepartment of Advanced Medicine for Respiratory Failure, Graduate School of Medicine, Kyoto University
bDepartment of Respiratory Medicine, Graduate School of Medicine, Kyoto University
cHealth Administration Center, University of Toyama
dFirst Department of Internal Medicine, Shinshu University School of Medicine
eThird Department of Internal Medicine, Faculty of Medical Sciences, University of Fukui
fDepartment of Radiology, Kanagawa Cardiovascular and Respiratory Center
gDepartment of Radiology, Kansai Rosai Hospital
hDepartment of Anatomic Pathology, Kurashiki Central Hospital
iClinical Research Center, National Hospital Organization Tokyo National Hospital
In 2011, comprehensive diagnostic criteria for IgG4-related disease were published in Japan. Organ-specific diagnostic criteria based on organ-specific findings were proposed and published by each of the related societies, and diagnostic criteria for IgG4-related respiratory disease were published in 2015. Based on revisions to the comprehensive diagnostic criteria in 2020 and the publication of the classification criteria, new diagnostic criteria for IgG4-related respiratory disease are presented. Emphasis is placed on the evaluation of specific pathological findings and the exclusion of other respiratory diseases. It is mentioned in the commentary that in cases with imaging findings suggestive of interstitial pneumonia with chronic fibrosis or a poor response to steroid therapy, other possible diseases should be considered.
Diagnostic criteria IgG4-related disease IgG4-related respiratory disease
Received 15 Feb 2023 / Accepted 24 Feb 2023
AJRS, 12(3): 109-113, 2023