Full Text of PDF (701k)
Article in Japanese
Abstract
Case Report
Primary systemic AL amyloidosis diagnosed in a case presenting with multiple nodular opacities of the lung
aDepartment of Internal Medicine (Pulmonology), Yamagata Prefectural Central Hospital
bDepartment of Internal Medicine (Hematology), Yamagata Prefectural Central Hospital
ABSTRACT
An 81-year-old man was found on chest CT to have multiple nodular opacities in the lungs. For the next three years, he was followed with no active treatment because he had no symptoms or signs, and his blood test results revealed no abnormalities. The multiple nodular opacities were found to be slowly enlarging and increasing in number; therefore bronchoscopy and transbronchial biopsy were performed, revealing AL amyloid. Further detailed examination led to the diagnosis of primary systemic AL amyloidosis (IgGλ type). The diffuse alveolar septal type of lung amyloidosis may sometimes manifest as multiple nodular opacities in the lung fields, and we report this rare case in which the detection of multiple nodular opacities in the lungs led to the diagnosis of systemic amyloidosis.
KEYWORDS
Pulmonary amyloidosis Primary systemic amyloidosis Multiple nodular opacities
Received 25 Sep 2016 ／ Accepted 21 Feb 2017
AJRS, 6(4): 249-254, 2017
Copyright © The Japanese Respiratory Society All Rights Reserved.