Pulmonary epithelioid hemangioendothelioma (PEH) is a rare neoplasm of endothelial origin that occasionally presents with multiple pulmonary nodules in young women. It has not yet been reported whether this disease affects pregnancy. A 34-year-old woman was referred to our hospital for further evaluation after multiple nodular shadows were detected on a chest X-ray at a medical checkup. She complained of no symptoms. The computed tomography showed multiple- and various-sized nodules up to 10 mm in diameter in the bilateral lung field. To obtain a detailed diagnosis, video-assisted thoracoscopic lung biopsy was performed. Upon histopathological examination, the center of the nodule was occupied by a hyalinized matrix, the periphery of the nodules showed intra-alveolar proliferation of the tumor cells, and immunohistochemical staining of these cells was positive for Factor-8-related antigen, CD31, and CD34. Therefore these pulmonary lesions were diagnosed pathologically as PEH. She became pregnant and gave birth; medical follow-ups continued without treatment for more than 5 years. Yet she still complained of no symptoms. This case suggests that PEH did not affect the pregnancy and delivery.