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Abstract
Case Report
A case of rapidly progressive interstitial pneumonia (RPIP) combined with clinically amyopathic dermatomyositis (CADM) successfully treated with intensive therapy
Shota Yokoyamaa Ken Satob Go Makimotob Hiroe Kayatanic Keiichi Fujiwarab Toshio Satob
aDepartment of General Medicine, National Hospital Organization Okayama Medical Center
bDepartment of Respiratory Medicine, National Hospital Organization Okayama Medical Center
cDepartment of Allergy and Respiratory Medicine, Okayama University Hospital
ABSTRACT
Clinically amyopathic dermatomyositis (CADM) is a subtype of dermatomyositis characterized by normal muscle enzyme levels and an absence of motor weakness, and it is frequently associated with interstitial pneumonia and a poor prognosis. We encountered a 62-year-old man with CADM who presented with dyspnea and rapidly progressive interstitial pneumonia. He was successfully treated with intensive therapy consisting of corticosteroid, cyclosporine A, and polymyxin B-immobilized fiber column hemoperfusion. CADM has a poor prognosis and should be treated promptly.
KEYWORDS
Dermatomyositis Clinically amyopathic dermatomyositis (CADM) Anti-KS antibody Rapidly progressive interstitial pneumonia (RPIP) Polymyxin B-immobilized fiber column hemoperfusion (PMX-DHP)
Received 12 Mar 2013 ／ Accepted 21 Jun 2013
AJRS, 2(6): 767-772, 2013
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