Full Text of PDF (719k)
Article in Japanese
Abstract
Case Report
A case of systemic sclerosis accompanied with spontaneous pneumothorax
Takahiro Hagaa Mizuki Fukuokaa Mizuo Moritaa Kohei Choa Hideyuki Kataokab Masatoshi Kuriharab
aDepartment of Respiratory Medicine, Nissan Tamagawa Hospital
bPneumothorax Research Center, Nissan Tamagawa Hosipital
ABSTRACT
The patient was a 16-year-old male who developed a left-sided spontaneous pneumothorax in October 2008 and a right-sided spontaneous pneumothorax in May 2010. He was referred to our hospital for recurrent pneumothorax in June 2010. A chest CT scan on admission showed several small cystic legions predominant in the bilateral lower lobes and a bulla in the right middle lobe. The operation was done by thoracoscopy, and the bulla in the right middle lobe was resected. A histological examination revealed a diffuse pulmonary interstitial infiltrate composed of lymphocyte and fibrosis accompanied with honeycomb. He was diagnosed with systemic sclerosis by sclerodermatous skin thickening of the hands and forearms and positive anti-Scl-70 antibody. Spontaneous pneumothorax is a rare complication in patients with systemic sclerosis and is thought to be a valuable case.
KEYWORDS
Systemic sclerosis Interstitial pneumonia Spontaneous pneumothorax
Received 11 Dec 2012 ／ Accepted 6 Feb 2013
AJRS, 2(4): 451-455, 2013
Copyright © The Japanese Respiratory Society All Rights Reserved.